Hello! First and foremost I would like to tell you what pulmonary hypertension(PH) means. It is the raise in blood pressure of the vessels within your lungs. There are various causes for PH - mainly heart diseases, chronic lung diseases, chronic pulmonary embolism , connective tissue diseases, interstitial lung diseases like sarcoidosis . Only if no such cause for Pulmonary hypertension is found then it is termed as Idiopathic Pulmonary hypertension. The most crucial thing is to ensure all tests are done to rule out these known causes of PH before stamping as Idiopathic co the treatment is entirely different. So pls do discuss with your physician regarding your diagnosis. Presuming you have been diagnosed right, treatment of IPAH (Idiopathic Pulmonary Arterial Hypertension) requires significant patient education regarding the available therapies and their potential complications. Management is best to be undertaken at centres with expertise in treating this rare disease. The drugs commonly used are calcium channel blockers , sildenafil, bosentan , prostacyclins. these dilate the Pulmonary vessel and reduce the pressure. As supportive measures anticoagulants, digoxin , diuretics, supplemental oxygen are prescribed in necessary cases. A low sodium low fluid diet is recommended in patients with volume overload. Single or double lung transplant is an option for patients who fail to respond to medical therapy. As far as the prognosis is concerned , although IPAH is a generally progressive and fatal disease , its prognosis is highly variable . Many patients characteristics correlate with prognosis including functional class, rapidity of onset and exercise capacity . Also there are various parameters of hemodynamic status of the patient and cardiac status that can predict the prognosis. There are occasional case reports which report patients to have survived for even 20 years with proper treatment . So kindly consult a qualified expert physician and get the right treatment .